Cystic lung in Marfan's syndrome.
نویسندگان
چکیده
Various pulmonary problems have been described in Marfan's syndrome. Unusual cystic lung changes in a young girl with Marfan's syndrome are described.
منابع مشابه
Ruptured Abdominal Aortic Aneurysm in Marfan's Syndrome.
A rare case of ruptured abdominal aortic aneurysm in Marfan's syndrome is described. The patient was treated successfully with a straight aortic tube graft. Histology of the aneurysm wall showed changes typical of cystic medial necrosis.
متن کاملCoexistence of fibromuscular dysplasia and cystic medial necrosis in a patient with Marfan's syndrome and bilateral carotid artery dissections.
BACKGROUND A primary arteriopathy is suspected in most patients with spontaneous dissections of the carotid artery, although the nature of this arteriopathy usually remains elusive. Angiographic changes of fibromuscular dysplasia (FMD), however, are found in 10% to 20% of patients with carotid dissections. CASE DESCRIPTION A 26-year-old woman with Marfan's syndrome presented with bilateral am...
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متن کاملUnruptured, isolated giant aneurysm of the sinus of valsalva resulting from medial mucoid degeneration.
We report a quite rare case of unruptured, isolated giant aneurysm of the sinus of Valsalva resulting from medial mucoid degeneration in a young adult woman. A 29-year-old Japanese female diagnosed as having an aneurysm of the sinus of Valsalva and severe aortic regurgitation with no clinical findings of Marfan's syndrome or Ehlers-Danlos syndrome. A modified Bentall's operation was performed s...
متن کاملCLINICOPATHOLOGIC CORRELATIONS Spontaneous Laceration of Ascending Aorta
Spontaneous laceration of the ascending aorta may result in (1) through-and-through laceration causing hemopericardium, (2) limited intramural dissection of blood (incomplete dissecting aneurysm), or (3) classical dissecting aneurysm. The latter is the most common manifestation. Background conditions include either extensive cystic medial necrosis (as may be seen in Marfan's syndrome) or hypert...
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عنوان ژورنال:
- Thorax
دوره 44 11 شماره
صفحات -
تاریخ انتشار 1989